Segmental ballistic movement overflow myoclonus: A clinical, electromyographic, and pharmacologic evaluation
Identifieur interne : 006125 ( Main/Exploration ); précédent : 006124; suivant : 006126Segmental ballistic movement overflow myoclonus: A clinical, electromyographic, and pharmacologic evaluation
Auteurs : J. Stübgen [Afrique du Sud] ; Lotz [Afrique du Sud]Source :
- Movement Disorders [ 0885-3185 ] ; 1991.
Descripteurs français
- Pascal (Inist)
English descriptors
- KwdEn :
- Adult, Ballistic movement overflow myoclonus, Biperiden (therapeutic use), Case study, Central nervous system, Cholinergic Fibers (drug effects), Cholinergic Fibers (physiology), Cholinergic disturbance, Computerized axial tomography, Drug response, Electrodiagnosis, Electromyography, Electromyography (drug effects), Exploration, Hemibalismus, Humans, Infusions, Intravenous, Male, Muscle Contraction (drug effects), Muscle Contraction (physiology), Muscles (innervation), Myoclonus, Myoclonus (drug therapy), Myoclonus (physiopathology), Neurologic Examination, Radiodiagnosis, Receptors, Cholinergic (drug effects), Receptors, Cholinergic (physiology), Treatment efficiency, Young adult.
- MESH :
- chemical , drug effects : Receptors, Cholinergic.
- chemical , physiology : Receptors, Cholinergic.
- chemical , therapeutic use : Biperiden.
- drug effects : Cholinergic Fibers, Electromyography, Muscle Contraction.
- drug therapy : Myoclonus.
- innervation : Muscles.
- physiology : Cholinergic Fibers, Muscle Contraction.
- physiopathology : Myoclonus.
- Adult, Humans, Infusions, Intravenous, Male, Neurologic Examination.
Abstract
A 27‐year‐old man presented with a sporadic, nonprogressive, right‐sided, segmental movement disorder that had started at the age of 2 years. Ballistic movement overflow myoclonus was diagnosed clinically and by surface electromyography. Special investigations did not detect anything except atrophy of the left temporal lobe on CT scan. The movement intensity was attenuated by alcohol but was minimally affected by high doses of oral propranolol (320 mg daily), clonazepam (36 mg daily), or trihexyphenidyl (32 mg daily). High‐dose intravenous biperidine (10 mg) resulted in dramatic improvement, but with unacceptable side effects. The possible role of a cholinergic disturbance in generating myoclonus is discussed.
Url:
DOI: 10.1002/mds.870060415
Affiliations:
Links toward previous steps (curation, corpus...)
- to stream Istex, to step Corpus: 003373
- to stream Istex, to step Curation: 003373
- to stream Istex, to step Checkpoint: 004268
- to stream PubMed, to step Corpus: 004E41
- to stream PubMed, to step Curation: 004E41
- to stream PubMed, to step Checkpoint: 004D93
- to stream Ncbi, to step Merge: 001D33
- to stream Ncbi, to step Curation: 001D33
- to stream Ncbi, to step Checkpoint: 001D33
- to stream Main, to step Merge: 009429
- to stream PascalFrancis, to step Corpus: 003782
- to stream PascalFrancis, to step Curation: 003042
- to stream PascalFrancis, to step Checkpoint: 003853
- to stream Main, to step Merge: 009525
- to stream Main, to step Curation: 006125
Le document en format XML
<record><TEI wicri:istexFullTextTei="biblStruct"><teiHeader><fileDesc><titleStmt><title xml:lang="en">Segmental ballistic movement overflow myoclonus: A clinical, electromyographic, and pharmacologic evaluation</title>
<author><name sortKey="Stubgen, J" sort="Stubgen, J" uniqKey="Stubgen J" first="J." last="Stübgen">J. Stübgen</name>
</author>
<author><name sortKey="Lotz" sort="Lotz" uniqKey="Lotz" last="Lotz">Lotz</name>
</author>
</titleStmt>
<publicationStmt><idno type="wicri:source">ISTEX</idno>
<idno type="RBID">ISTEX:FD82B6B0535553A995DE84CEDF512FDC6E98A34F</idno>
<date when="1991" year="1991">1991</date>
<idno type="doi">10.1002/mds.870060415</idno>
<idno type="url">https://api.istex.fr/document/FD82B6B0535553A995DE84CEDF512FDC6E98A34F/fulltext/pdf</idno>
<idno type="wicri:Area/Istex/Corpus">003373</idno>
<idno type="wicri:Area/Istex/Curation">003373</idno>
<idno type="wicri:Area/Istex/Checkpoint">004268</idno>
<idno type="wicri:doubleKey">0885-3185:1991:Stubgen J:segmental:ballistic:movement</idno>
<idno type="wicri:source">PubMed</idno>
<idno type="RBID">pubmed:1758455</idno>
<idno type="wicri:Area/PubMed/Corpus">004E41</idno>
<idno type="wicri:Area/PubMed/Curation">004E41</idno>
<idno type="wicri:Area/PubMed/Checkpoint">004D93</idno>
<idno type="wicri:Area/Ncbi/Merge">001D33</idno>
<idno type="wicri:Area/Ncbi/Curation">001D33</idno>
<idno type="wicri:Area/Ncbi/Checkpoint">001D33</idno>
<idno type="wicri:doubleKey">0885-3185:1991:Stubgen J:segmental:ballistic:movement</idno>
<idno type="wicri:Area/Main/Merge">009429</idno>
<idno type="wicri:source">INIST</idno>
<idno type="RBID">Pascal:93-0155512</idno>
<idno type="wicri:Area/PascalFrancis/Corpus">003782</idno>
<idno type="wicri:Area/PascalFrancis/Curation">003042</idno>
<idno type="wicri:Area/PascalFrancis/Checkpoint">003853</idno>
<idno type="wicri:doubleKey">0885-3185:1991:Stubgen J:segmental:ballistic:movement</idno>
<idno type="wicri:Area/Main/Merge">009525</idno>
<idno type="wicri:Area/Main/Curation">006125</idno>
<idno type="wicri:Area/Main/Exploration">006125</idno>
</publicationStmt>
<sourceDesc><biblStruct><analytic><title level="a" type="main" xml:lang="en">Segmental ballistic movement overflow myoclonus: A clinical, electromyographic, and pharmacologic evaluation</title>
<author><name sortKey="Stubgen, J" sort="Stubgen, J" uniqKey="Stubgen J" first="J." last="Stübgen">J. Stübgen</name>
<affiliation wicri:level="1"><country xml:lang="fr">Afrique du Sud</country>
<wicri:regionArea>Department of Neurology, H. F. Verwoerd Hospital, University of Pretoria</wicri:regionArea>
<wicri:noRegion>University of Pretoria</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Lotz" sort="Lotz" uniqKey="Lotz" last="Lotz">Lotz</name>
<affiliation wicri:level="1"><country xml:lang="fr">Afrique du Sud</country>
<wicri:regionArea>Department of Neurology, H. F. Verwoerd Hospital, University of Pretoria</wicri:regionArea>
<wicri:noRegion>University of Pretoria</wicri:noRegion>
</affiliation>
<affiliation><wicri:noCountry code="subField">0001</wicri:noCountry>
</affiliation>
</author>
</analytic>
<monogr></monogr>
<series><title level="j">Movement Disorders</title>
<title level="j" type="sub">Official Journal of the Movement Disorder Society</title>
<title level="j" type="abbrev">Mov. Disord.</title>
<idno type="ISSN">0885-3185</idno>
<idno type="eISSN">1531-8257</idno>
<imprint><publisher>Wiley Subscription Services, Inc., A Wiley Company</publisher>
<pubPlace>Hoboken</pubPlace>
<date type="published" when="1991">1991</date>
<biblScope unit="vol">6</biblScope>
<biblScope unit="issue">4</biblScope>
<biblScope unit="page" from="350">350</biblScope>
<biblScope unit="page" to="353">353</biblScope>
</imprint>
<idno type="ISSN">0885-3185</idno>
</series>
<idno type="istex">FD82B6B0535553A995DE84CEDF512FDC6E98A34F</idno>
<idno type="DOI">10.1002/mds.870060415</idno>
<idno type="ArticleID">MDS870060415</idno>
</biblStruct>
</sourceDesc>
<seriesStmt><idno type="ISSN">0885-3185</idno>
</seriesStmt>
</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Adult</term>
<term>Ballistic movement overflow myoclonus</term>
<term>Biperiden (therapeutic use)</term>
<term>Case study</term>
<term>Central nervous system</term>
<term>Cholinergic Fibers (drug effects)</term>
<term>Cholinergic Fibers (physiology)</term>
<term>Cholinergic disturbance</term>
<term>Computerized axial tomography</term>
<term>Drug response</term>
<term>Electrodiagnosis</term>
<term>Electromyography</term>
<term>Electromyography (drug effects)</term>
<term>Exploration</term>
<term>Hemibalismus</term>
<term>Humans</term>
<term>Infusions, Intravenous</term>
<term>Male</term>
<term>Muscle Contraction (drug effects)</term>
<term>Muscle Contraction (physiology)</term>
<term>Muscles (innervation)</term>
<term>Myoclonus</term>
<term>Myoclonus (drug therapy)</term>
<term>Myoclonus (physiopathology)</term>
<term>Neurologic Examination</term>
<term>Radiodiagnosis</term>
<term>Receptors, Cholinergic (drug effects)</term>
<term>Receptors, Cholinergic (physiology)</term>
<term>Treatment efficiency</term>
<term>Young adult</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="drug effects" xml:lang="en"><term>Receptors, Cholinergic</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="physiology" xml:lang="en"><term>Receptors, Cholinergic</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="therapeutic use" xml:lang="en"><term>Biperiden</term>
</keywords>
<keywords scheme="MESH" qualifier="drug effects" xml:lang="en"><term>Cholinergic Fibers</term>
<term>Electromyography</term>
<term>Muscle Contraction</term>
</keywords>
<keywords scheme="MESH" qualifier="drug therapy" xml:lang="en"><term>Myoclonus</term>
</keywords>
<keywords scheme="MESH" qualifier="innervation" xml:lang="en"><term>Muscles</term>
</keywords>
<keywords scheme="MESH" qualifier="physiology" xml:lang="en"><term>Cholinergic Fibers</term>
<term>Muscle Contraction</term>
</keywords>
<keywords scheme="MESH" qualifier="physiopathology" xml:lang="en"><term>Myoclonus</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Adult</term>
<term>Humans</term>
<term>Infusions, Intravenous</term>
<term>Male</term>
<term>Neurologic Examination</term>
</keywords>
<keywords scheme="Pascal" xml:lang="fr"><term>Adulte jeune</term>
<term>Efficacité traitement</term>
<term>Electrodiagnostic</term>
<term>Electromyographie</term>
<term>Etude cas</term>
<term>Exploration</term>
<term>Hémiballisme</term>
<term>Myoclonie</term>
<term>Radiodiagnostic</term>
<term>Système nerveux central</term>
<term>Tomodensitométrie</term>
</keywords>
</textClass>
<langUsage><language ident="en">en</language>
</langUsage>
</profileDesc>
</teiHeader>
<front><div type="abstract" xml:lang="en">A 27‐year‐old man presented with a sporadic, nonprogressive, right‐sided, segmental movement disorder that had started at the age of 2 years. Ballistic movement overflow myoclonus was diagnosed clinically and by surface electromyography. Special investigations did not detect anything except atrophy of the left temporal lobe on CT scan. The movement intensity was attenuated by alcohol but was minimally affected by high doses of oral propranolol (320 mg daily), clonazepam (36 mg daily), or trihexyphenidyl (32 mg daily). High‐dose intravenous biperidine (10 mg) resulted in dramatic improvement, but with unacceptable side effects. The possible role of a cholinergic disturbance in generating myoclonus is discussed.</div>
</front>
</TEI>
<affiliations><list><country><li>Afrique du Sud</li>
</country>
</list>
<tree><country name="Afrique du Sud"><noRegion><name sortKey="Stubgen, J" sort="Stubgen, J" uniqKey="Stubgen J" first="J." last="Stübgen">J. Stübgen</name>
</noRegion>
<name sortKey="Lotz" sort="Lotz" uniqKey="Lotz" last="Lotz">Lotz</name>
</country>
</tree>
</affiliations>
</record>
Pour manipuler ce document sous Unix (Dilib)
EXPLOR_STEP=$WICRI_ROOT/Wicri/Santé/explor/MovDisordV3/Data/Main/Exploration
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 006125 | SxmlIndent | more
Ou
HfdSelect -h $EXPLOR_AREA/Data/Main/Exploration/biblio.hfd -nk 006125 | SxmlIndent | more
Pour mettre un lien sur cette page dans le réseau Wicri
{{Explor lien |wiki= Wicri/Santé |area= MovDisordV3 |flux= Main |étape= Exploration |type= RBID |clé= ISTEX:FD82B6B0535553A995DE84CEDF512FDC6E98A34F |texte= Segmental ballistic movement overflow myoclonus: A clinical, electromyographic, and pharmacologic evaluation }}
This area was generated with Dilib version V0.6.23. |